Elaborates Congenital Aortic Stenosis in details?

More common in males (4: 1). High incidence of Bicuspid Aortic valve. Murmur present from early infancy and sometimes at birth if severe AS is present. Present with LV failure in neonatal period in severe case. Supravalvular AS is associated with Congenital Rubella syndrome and William Syndrome. Effort dyspnea, syncope and fatigue reflect an inadequate increment in cardiac output.

High risk of sudden death especially in adolescent and young adults. Angina Pectoris can occur in young patients. The murmur of AS is loudest over the ascending aorta (i.e. upper right sternal border (URSB) or aortic valve area). LVH in ECG.

Figure: Congenital aortic stenosis