Reference no: EM132818475
1. Tyr is not an essential amino acid. Based on the PAH reaction, how do you know that Tyr is not an essential amino acid? Be very specific.
2. In a person with PKU, what do you predict about Phe levels? Will they be elevated, reduced or unchanged?
3. In a person with PKU, what do you predict about Tyr levels? Will they be elevated, reduced or unchanged?
4. In a person with PKU, do you predict Tyr to be essential or non-essential? Explain your answer. (Hint: in a person with PKU, can Tyr still be made from Phe?)
5. Do people with PKU need ANY Phe? Why or why not?
6. What is the source of Phe for people who are strictly following the PKU diet?
7. Which match with which
PAH substrate
BH4 enzyme
Phe product
Tyr cofactor